Epidermolysis Bullosa
Description General and supportive measures Referral ICD-10 Code: Q81.9 DESCRIPTION Congenital, hereditary blistering skin lesions with onset in the newborn. Lesions have an erythematous base. Involvement of the mucous membranes as well as loss of nails may occur. GENERAL AND SUPPORTIVE MEASURES May require monitoring in a high or intensive care unit. Aseptic aspiration of bullae on th
General and supportive measures
ICD-10 Code: Q81.9
DESCRIPTION
Congenital, hereditary blistering skin lesions with onset in the newborn. Lesions have an erythematous base. Involvement of the mucous membranes as well as loss of nails may occur.
GENERAL AND SUPPORTIVE MEASURES
- May require monitoring in a high or intensive care unit.
- Aseptic aspiration of bullae on the side can be performed to relieve pressure (ensure the roof of the blister remains intact to protect underlying skin).
- Prevent infection with appropriate wound care.
- Attend to fluid and nutrition balance.
Important to manage baseline pain and procedural pain, see Pain Control.
REFERRAL
- All cases for biopsy, classification of type and management plan.
Standard Treatment Guidelines And Essential Medicines List For South Africa, Hospital Level, Paediatrics, 2023 Edition
Chapter 5: Dermatology, 5.1 Bullae, 5.1.1 Epidermolysis Bullosa