E70-E90
Metabolic disorders
- E70.0Classical phenylketonuria
- E70.1Other hyperphenylalaninaemias
- E70.2Disorders of tyrosine metabolism
- E70.3Albinism
- E70.8Other disorders of aromatic amino-acid metabolism
- E70.9Disorder of aromatic amino-acid metabolism, unspecified
- E71.0Maple-syrup-urine disease
- E71.1Other disorders of branched-chain amino-acid metabolism
- E71.2Disorder of branched-chain amino-acid metabolism, unspecified
- E71.3Disorders of fatty-acid metabolism
- E72.0Disorders of amino-acid transport
- E72.1Disorders of sulfur-bearing amino-acid metabolism
- E72.2Disorders of urea cycle metabolism
- E72.3Disorders of lysine and hydroxylysine metabolism
- E72.4Disorders of ornithine metabolism
- E72.5Disorders of glycine metabolism
- E72.8Other specified disorders of amino-acid metabolism
- E72.9Disorder of amino-acid metabolism, unspecified
- E73.0Congenital lactase deficiency
- E73.1Secondary lactase deficiency
- E73.8Other lactose intolerance
- E73.9Lactose intolerance, unspecified
- E74.0Glycogen storage disease
- E74.1Disorders of fructose metabolism
- E74.2Disorders of galactose metabolism
- E74.3Other disorders of intestinal carbohydrate absorption
- E74.4Disorders of pyruvate metabolism and gluconeogenesis
- E74.8Other specified disorders of carbohydrate metabolism
- E74.9Disorder of carbohydrate metabolism, unspecified
- E75.0GM2 gangliosidosis
- E75.1Other gangliosidosis
- E75.2Other sphingolipidosis
- E75.3Sphingolipidosis, unspecified
- E75.4Neuronal ceroid lipofuscinosis
- E75.5Other lipid storage disorders
- E75.6Lipid storage disorder, unspecified
- E76.0Mucopolysaccharidosis, type I
- E76.1Mucopolysaccharidosis, type Il
- E76.2Other mucopolysaccharidoses
- E76.3Mucopolysaccharidosis, unspecified
- E76.8Other disorders of glucosaminoglycan metabolism
- E76.9Disorder of glucosaminoglycan metabolism, unspecified
- E77.0Defects in post-translational modification of lysosomal enzymes
- E77.1Defects in glycoprotein degradation
- E77.8Other disorders of glycoprotein metabolism
- E77.9Disorder of glycoprotein metabolism, unspecified
- E78.0Pure hypercholesterolaemia
- E78.1Pure hyperglyceridaemia
- E78.2Mixed hyperlipidaemia
- E78.3Hyperchylomicronaemia
- E78.4Other hyperlipidaemia
- E78.5Hyperlipidaemia, unspecified
- E78.6Lipoprotein deficiency
- E78.8Other disorders of lipoprotein metabolism
- E78.9Disorder of lipoprotein metabolism, unspecified
- E79.0Hyperuricaemia without signs of inflammatory arthritis and tophaceous disease
- E79.1Lesch-Nyhan syndrome
- E79.8Other disorders of purine and pyrimidine metabolism
- E79.9Disorder of purine and pyrimidine metabolism, unspecified
- E80.0Hereditary erythropoietic porphyria
- E80.1Porphyria cutanea tarda
- E80.2Other porphyria
- E80.3Defects of catalase and peroxidase
- E80.4Gilbert's syndrome
- E80.5Crigler-Najjar syndrome
- E80.6Other disorders of bilirubin metabolism
- E80.7Disorder of bilirubin metabolism, unspecified
- E83.0Disorders of copper metabolism
- E83.1Disorders of iron metabolism
- E83.2Disorders of zinc metabolism
- E83.3Disorders of phosphorus metabolism and phosphatases
- E83.4Disorders of magnesium metabolism
- E83.5Disorders of calcium metabolism
- E83.8Other disorders of mineral metabolism
- E83.9Disorder of mineral metabolism, unspecified
- E84.0Cystic fibrosis with pulmonary manifestations
- E84.1Cystic fibrosis with intestinal manifestations
- E84.8Cystic fibrosis with other manifestations
- E84.9Cystic fibrosis, unspecified
- E85.0Non-neuropathic heredofamilial amyloidosis
- E85.1Neuropathic heredofamilial amyloidosis
- E85.2Heredofamilial amyloidosis, unspecified
- E85.3Secondary systemic amyloidosis
- E85.4Organ-limited amyloidosis
- E85.8Other amyloidosis
- E85.9Amyloidosis, unspecified
- E86Volume depletion
- E87.0Hyperosmolality and hypernatraemia
- E87.1Hypo-osmolality and hyponatraemia
- E87.2Acidosis
- E87.3Alkalosis
- E87.4Mixed disorder of acid-base balance
- E87.5Hyperkalaemia
- E87.6Hypokalaemia
- E87.7Fluid overload
- E87.8Other disorders of electrolyte and fluid balance, not elsewhere classified
- E88.0Disorders of plasma-protein metabolism, not elsewhere classified
- E88.1Lipodystrophy, not elsewhere classified
- E88.2Lipomatosis, not elsewhere classified
- E88.3Tumour lysis syndrome
- E88.8Other specified metabolic disorders
- E88.9Metabolic disorder, unspecified
- E89.0Postprocedural hypothyroidism
- E89.1Postprocedural hypoinsulinaemia
- E89.2Postprocedural hypoparathyroidism
- E89.3Postprocedural hypopituitarism
- E89.4Postprocedural ovarian failure
- E89.5Postprocedural testicular hypofunction
- E89.6Postprocedural adrenocortical(-medullary) hypofunction
- E89.8Other postprocedural endocrine and metabolic disorders
- E89.9Postprocedural endocrine and metabolic disorder, unspecified
- E90Nutritional and metabolic disorders in diseases classified elsewhere